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Aneurysmformation may develop independently of disease activityin WG and may be unpredictable, so that a carefulobservation whether aneurysm is formed should be continuouslyconsidered in the follow-up during the entire course.", "subitem_description_type": "Other"}]}, "item_2_description_15": {"attribute_name": "表示順", "attribute_value_mlt": [{"subitem_description": "18", "subitem_description_type": "Other"}]}, "item_2_description_16": {"attribute_name": "アクセション番号", "attribute_value_mlt": [{"subitem_description": "KJ00007071079", "subitem_description_type": "Other"}]}, "item_2_description_8": {"attribute_name": "記事種別(日)", "attribute_value_mlt": [{"subitem_description": "症例報告", "subitem_description_type": "Other"}]}, "item_2_description_9": {"attribute_name": "記事種別(英)", "attribute_value_mlt": [{"subitem_description": "Case Report", "subitem_description_type": "Other"}]}, "item_2_source_id_1": {"attribute_name": "雑誌書誌ID", "attribute_value_mlt": [{"subitem_source_identifier": "AA00629581", 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"Department of Cardiovascular Medicine, Dokkyo Medical University Nikko Medical Center"}, {"subitem_text_language": "en", "subitem_text_value": "Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine"}, {"subitem_text_language": "en", "subitem_text_value": "Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine"}, {"subitem_text_language": "en", "subitem_text_value": "Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine"}, {"subitem_text_language": "en", "subitem_text_value": "Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine"}]}, "item_2_title_3": {"attribute_name": "論文名よみ", "attribute_value_mlt": [{"subitem_title": "キョウブ カコウ ダイドウミャク ニ ドウミャクリュウ オ ガッペイシタ Wegener ニクガシュ ショウ ノ 1レイ "}]}, "item_creator": {"attribute_name": "著者", "attribute_type": "creator", "attribute_value_mlt": 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"subitem_subject_scheme": "Other"}, {"subitem_subject": "PR3-ANCA( C-ANCA)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Wegener 肉芽腫症", "subitem_subject_scheme": "Other"}, {"subitem_subject": "aortic aneurysm", "subitem_subject_language": "en", "subitem_subject_scheme": "Other"}, {"subitem_subject": "PR3-ANCA( C-ANCA)", "subitem_subject_language": "en", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Wegener\u0027s granulomatosis", "subitem_subject_language": "en", "subitem_subject_scheme": "Other"}]}, "item_language": {"attribute_name": "言語", "attribute_value_mlt": [{"subitem_language": "jpn"}]}, "item_resource_type": {"attribute_name": "資源タイプ", "attribute_value_mlt": [{"resourcetype": "journal article", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_title": "胸部下行大動脈に動脈瘤を合併したWegener 肉芽腫症の1 例", "item_titles": {"attribute_name": "タイトル", "attribute_value_mlt": [{"subitem_title": "胸部下行大動脈に動脈瘤を合併したWegener 肉芽腫症の1 例"}, {"subitem_title": "A Case Aneurysm on the Descending Thoracic Aorta in Wegener\u0027s Granulomatosis", "subitem_title_language": "en"}]}, "item_type_id": "2", "owner": "3", "path": ["57"], "permalink_uri": "https://dmu.repo.nii.ac.jp/records/932", "pubdate": {"attribute_name": "公開日", "attribute_value": "2017-05-24"}, "publish_date": "2017-05-24", "publish_status": "0", "recid": "932", "relation": {}, "relation_version_is_last": true, "title": ["胸部下行大動脈に動脈瘤を合併したWegener 肉芽腫症の1 例"], "weko_shared_id": 3}
  1. Dokkyo Journal of Medical Sciences
  2. 38(1) 2011

胸部下行大動脈に動脈瘤を合併したWegener 肉芽腫症の1 例

https://dmu.repo.nii.ac.jp/records/932
https://dmu.repo.nii.ac.jp/records/932
374f6881-ca31-49d6-b2b9-fbc022f23f2e
名前 / ファイル ライセンス アクション
KJ00007071079.pdf KJ00007071079.pdf (502.1 kB)
Item type [ELS]学術雑誌論文 / Journal Article(1)
公開日 2017-05-24
タイトル
タイトル 胸部下行大動脈に動脈瘤を合併したWegener 肉芽腫症の1 例
タイトル
言語 en
タイトル A Case Aneurysm on the Descending Thoracic Aorta in Wegener's Granulomatosis
言語
言語 jpn
キーワード
主題 大動脈瘤
キーワード
主題 PR3-ANCA( C-ANCA)
キーワード
主題 Wegener 肉芽腫症
キーワード
言語 en
主題 aortic aneurysm
キーワード
言語 en
主題 PR3-ANCA( C-ANCA)
キーワード
言語 en
主題 Wegener's granulomatosis
資源タイプ
資源タイプ識別子 http://purl.org/coar/resource_type/c_6501
資源タイプ journal article
雑誌書誌ID
収録物識別子 AA00629581
論文名よみ
タイトル キョウブ カコウ ダイドウミャク ニ ドウミャクリュウ オ ガッペイシタ Wegener ニクガシュ ショウ ノ 1レイ
著者 戸田, 正夫

× 戸田, 正夫

WEKO 4209

戸田, 正夫

ja-Kana トダ, マサオ

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増田, 浩之

× 増田, 浩之

WEKO 4210

増田, 浩之

ja-Kana マスダ, ヒロユキ

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田中, 彩絵

× 田中, 彩絵

WEKO 4211

田中, 彩絵

ja-Kana タナカ, アヤエ

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大西, 祥五

× 大西, 祥五

WEKO 4212

大西, 祥五

ja-Kana オオニシ, ショウゴ

Search repository
鹿島, 隆一

× 鹿島, 隆一

WEKO 4213

鹿島, 隆一

ja-Kana カシマ, リュウイチ

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町田, 優

× 町田, 優

WEKO 4214

町田, 優

ja-Kana マチダ, マサル

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原澤, 寛

× 原澤, 寛

WEKO 4215

原澤, 寛

ja-Kana ハラサワ, ヒロシ

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中元, 隆明

× 中元, 隆明

WEKO 4216

中元, 隆明

ja-Kana ナカモト, タカアキ

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池野, 義彦

× 池野, 義彦

WEKO 4217

池野, 義彦

ja-Kana イケノ, ヨシヒコ

Search repository
梅津, 貴史

× 梅津, 貴史

WEKO 4218

梅津, 貴史

ja-Kana ウメズ, タカフミ

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倉沢, 和宏

× 倉沢, 和宏

WEKO 4219

倉沢, 和宏

ja-Kana クラサワ, カズヒロ

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福田, 健

× 福田, 健

WEKO 4220

福田, 健

ja-Kana フクダ, タケシ

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Toda, Masao

× Toda, Masao

WEKO 4221

en Toda, Masao

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Masuda, Hiroyuki

× Masuda, Hiroyuki

WEKO 4222

en Masuda, Hiroyuki

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Tanaka, Ayae

× Tanaka, Ayae

WEKO 4223

en Tanaka, Ayae

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Chnishi, Shogo

× Chnishi, Shogo

WEKO 4224

en Chnishi, Shogo

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Kashima, Ryuichi

× Kashima, Ryuichi

WEKO 4225

en Kashima, Ryuichi

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Masaru, Machida

× Masaru, Machida

WEKO 4226

en Masaru, Machida

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Harasawa, Hiroshi

× Harasawa, Hiroshi

WEKO 4227

en Harasawa, Hiroshi

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Nakamoto, Takaaki

× Nakamoto, Takaaki

WEKO 4228

en Nakamoto, Takaaki

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Ikeno, Yoshihiko

× Ikeno, Yoshihiko

WEKO 4229

en Ikeno, Yoshihiko

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Umezu, Takafumi

× Umezu, Takafumi

WEKO 4230

en Umezu, Takafumi

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Kurasawa, Kazuhiro

× Kurasawa, Kazuhiro

WEKO 4231

en Kurasawa, Kazuhiro

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Fukuda, Takeshi

× Fukuda, Takeshi

WEKO 4232

en Fukuda, Takeshi

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著者所属(日)
獨協医科大学日光医療センター膠原病・アレルギー内科
著者所属(日)
獨協医科大学日光医療センター呼吸器内科
著者所属(日)
獨協医科大学内科学(呼吸器・アレルギー)
著者所属(日)
獨協医科大学日光医療センター呼吸器内科
著者所属(日)
獨協医科大学日光医療センター呼吸器内科
著者所属(日)
獨協医科大学日光医療センター呼吸器内科
著者所属(日)
獨協医科大学日光医療センター呼吸器内科
著者所属(日)
獨協医科大学日光医療センター循環器内科
著者所属(日)
獨協医科大学内科学(呼吸器・アレルギー)
著者所属(日)
獨協医科大学内科学(呼吸器・アレルギー)
著者所属(日)
獨協医科大学内科学(呼吸器・アレルギー)
著者所属(日)
獨協医科大学内科学(呼吸器・アレルギー)
著者所属(英)
en
Department of Rheumatology and Clinical Immunology, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Cardiovascular Medicine, Dokkyo Medical University Nikko Medical Center
著者所属(英)
en
Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine
著者所属(英)
en
Department of Respiratory Medicine and Clinical Immunology, Dokkyo Medical University School of Medicine
記事種別(日)
内容記述タイプ Other
内容記述 症例報告
記事種別(英)
内容記述タイプ Other
内容記述 Case Report
抄録(日)
内容記述タイプ Other
内容記述 79 歳男性.発熱,咳嗽で発症し,鼻閉の既往,空洞を伴う両下肺の浸潤影,顕微鏡的血尿,急速進行する腎機能障害およびPR3-ANCA 高値を示し,Wegener 肉芽腫症( WG) と診断された.一時シクロフォスファミド併用を含む,高用量副腎ステロイド療法が開始され,臨床および検査所見は改善した.ステロイド薬は漸減され,3 ヶ月後にはC-ANCA は陰性化した.WG は寛解していたが,8 ヶ月後に胸部下行大動脈瘤形成を認め,その1 ヶ月後に突然大喀血し,死亡した.動脈瘤形成は疾患活動性とは関連なく,経過中注意深い観察の継続を要する.
抄録(英)
内容記述タイプ Other
内容記述 A 79-year-old man was admitted because of fever andcough. He had been diagnosed with Wegener's granulomatosis(WG) on the basis of 10-year history of stuffy nose,pulmonary infiltrates with cavity formation, rapidly progressedrenal dysfunction with microscopic hematuria, andhigh level of PR3-ANCA. He was treated with high dose ofglucocorticoid( GC) temporarily in combination with cyclophosphamide,accordingly, the clinical manifestation and thelaboratory results had been recovering. The dose of GC wastapered down, and 3 months after the initiation of therapy,C-ANCA testing was negative. Despite remission was obtained,8 months after, chest computed tomography (CT)scan showed aneurysm formation on the descending aorta.One month after that, the patient had an abrupt onset ofcoughing up a massive amount of blood, and died. Aneurysmformation may develop independently of disease activityin WG and may be unpredictable, so that a carefulobservation whether aneurysm is formed should be continuouslyconsidered in the follow-up during the entire course.
書誌情報 Dokkyo journal of medical sciences

巻 38, 号 1, p. 119-126, 発行日 2011-03-25
ISSN
収録物識別子 03855023
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